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Blood Coagul Fibrinolysis ; 26(8): 964-6, 2015 Dec.
Artigo em Inglês | MEDLINE | ID: mdl-26397882

RESUMO

Acquired haemophilia A (AHA) is a life-threatening haemorrhagic disorder that occurs with various underlying conditions such as autoimmune disease, drug reactions, lymphoproliferative diseases, solid tumours and pregnancy/postpartum status. However, in half of all reported cases, the underlying disease is unknown. Most AHA cases develop in adults; paediatric/adolescent cases are extremely rare. The main clinical symptom is bleeding into the skin, muscles, soft tissues and/or mucous membranes. Here, we report the case of an otherwise healthy 12-year-old girl who presented with prolonged bleeding postexodontia. After being diagnosed with AHA, she was successfully treated with recombinant activated factor VII infusion and oral prednisolone. To avoid such unanticipated bleeding when performing dental extraction, preoperative haemostatic screening tests are recommended.


Assuntos
Exsanguinação/tratamento farmacológico , Hemofilia A/tratamento farmacológico , Extração Dentária/efeitos adversos , Criança , Exsanguinação/sangue , Exsanguinação/etiologia , Exsanguinação/patologia , Fator VIIa/uso terapêutico , Feminino , Hemofilia A/sangue , Hemofilia A/etiologia , Hemofilia A/patologia , Hemostáticos/uso terapêutico , Humanos , Prednisolona/uso terapêutico , Proteínas Recombinantes/uso terapêutico , Resultado do Tratamento
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